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Familial Hemiplegic Migraine and Autosomal Dominant Arteriopathy with Leukoencephalopathy (CADASIL)
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Clinical Spectrum of CADASIL:A Study of 7 Families
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Genetic Causes of Cerebral Small Vessel Diseases, A Parctical Guide for Neurologists
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Ears of the Lynx Magnetic Resonance Imaging Sign
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Limbic-Predominant Age-Related TDP-43 Encephalopathy (LATE): Consensus Working Group Report
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Clinicopathologic Conference, Primary Progressive Aphasia, Semantic Variant, due to TAR DNA Binding Protein 43 associated Frontotemporal Lobar Degen
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A 54-year-old woman with Dementia, Myoclonus, and Ataxia
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Amyotrophic Lateral Sclerosis
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A Young Man with Progressive Language Difficulty and Early-Onset Dementia
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Clinicopathologic Conference, Frontotemporal Lobar Degeneration with Tau-positive Inclusions (Picks Disease Subtype) Due to a Gly389Arg MAPT Mutation, Resulting in the Behavioral Variant of Frontotemporal Dementia with Parkinsonism
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Development of a Suspicion Index to Aid Diagnosis of Niemann-Pick Disease Type C
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Fully-Automated Quantification of Regional Brain Volumes for Improved Detection of Focal Atrophy in Alzheimers Disease
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Progressive Supranuclear Palsy: A Current Review
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Cerebral Cortical and White Matter Lesions in Amyotrophic Lateral Sclerosis With Dementia; Correlation With MR and Pathologic Examinations
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Dementia and White-Matter Demyelination in Young Patient With Neurosyphilis
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Vascular Parkinsonism and Dementia in a CADASIL Case with Intact Nigrostriatal Dopaminergic System
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Cerebral Autosomal Dominant Arteriopathy With Subcortical Infarcts and Leukoencephalopathy (CADASIL)
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A Practical Approach to the Diagnosis and Management of MELAS: Case Report and Review
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Clinicopath Conf., Pick's Disease, Case 11-2000
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Medial Temporal Lobe Atrophy on MRI in Dementia with Lewy Bodies
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Low Body Weight in Alzheimer's Disease is Associated with Mesial Temporal Cortex Atrophy
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Autosomal Dominant Migraine with MRI White-Matter Abnormalities Mapping to the CADASIL Locus
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Mitochondrial DNA and Disease
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Progress in the Genetics of Cerebrovascular Disease Inherited Subcortical Arteriopathies
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Progressive Supranuclear Palsy:Neuropathologic and Clinical Heterogeneity
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Niemann-Pick Disease Type C:Diagnosis and Outcome in Children, with Particular Reference to Liver disease
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A Familial Disorder with Subcortical Ischemic Strokes, Dementia, and Leukoencephalopathy
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The Clinical Features & Natural History of the Steele-Richardson-Olszewski Syndrome (Prog Supranuclear Palsy)
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Classic & Generalized Variants of Pick's Disease, A Clinicopath, Ultrastruc & Immunocyto Study
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Clinical Features of Subcortical Arteriosclerotic Encephalopathy (Binswanger Disease)
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Whipple's Disease with Predominating Neuro-ophthalmic Manifestations
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Neuro-Behcet Disease:Two Cases & Neuroradiologic Findings
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Infiltration of the Leptomeninges by Systemic Cancer:a Clinical & Pathologic Study
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Cerebral Vascular Disease & Behavior
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Whipple's Disease & Papilledema
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A 17-Year-Old Girl with Progressive Cognitive Impairment
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Adults with Cerebral Palsy Require Ongoing Neurologic Care
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Chronic Meningitis
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Immunocompetent Patient with Multiple Cranial Nerve Palsies, Ataxia, and Cognitive Decline
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Clinicopathologic Conference, Creutzfeldt-Jakob Disease
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Antibody-Mediated Encephalitis
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Pantothenate Kinase - Associated Neurodegeneration (PKAN)
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Clinicopathologic Conference, MELAS (mitochondrial encephalopathy, lactic acidosis, and stroke like episodes)
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Precipitous Deterioration of Motor Function, Cognition, and Behavior
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A 40-year old Woman with Difficulty Going Down Stairs in High-Heeled Shoes
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Diseases of the Nervous System Caused by Nutritional Deficiency, Vitamin B12 (Cobalamin) Deficiency (Subacute Combined Degeneration)
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Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Subacute Sclerosing Panencephalitis
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Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Progressive Rubella Panencephalitis
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